Isolated congenital megacystis with spontaneous resolution: an exceedingly rare entity.
نویسنده
چکیده
INTRODUCTION Megacystisisarareconditionininfants,whichisusuallyassociatedwithrefluxing megaureters,prune-bellysyndrome(PBS),infravesicalobstructionorpresents as themegacystismicrocolon intestinal hypoperistalsis syndrome (MMIHS). Rarereven,isisolatedcongenitalmegacystis(ICM).Theetiologyofthisentityisunknown. Myentericplexuspathology(1)andamildformofMMIHS(2)havebeenproposedasplausible pathologies.Hereweaddanothercasethatresolvedspontaneously.
منابع مشابه
Megacystis Megacolon Intestinal Hypoperistalsis Syndrome: A Rare Entity!
Megacystis microcolon intestinal hypoperistalsis syndrome (MMIHS) is now a well established entity [1,2]. Also known as Berdon syndrome [1], it is characterized by massive abdominal distension caused by a largely dilated non obstructed urinary bladder, microcolon and decreased or absent intestinal peristalsis. Isolated cases of congenital megacystis [3,4] and microcolon without megacystis [5] h...
متن کاملIsolated congenital megacystis with spontaneous resolution: a case report.
The patient was a male infant with an antenatal diagnosis of huge intraabdominal mass. Prenatal ultrasound at 35 weeks gestation revealed a markedly enlarged cystic mass in the lower abdomen. After birth at 38 weeks, the infant was allowed to void spontaneously and passed meconium. Ultrasonography showed an enlarged bladder with wall thickness of 2.9 mm and no hydronephrosis. Voiding cystoureth...
متن کاملMegacystis-Microcolon-Intestinal Hypoperistalsis Syndrome Associated With Prune Belly Syndrome: A Case Report
Megacystis Microcolon Intestinal Hypoperistalsis Syndrome is a quite rare congenital anomaly that presents with a functional obstruction of the gastrointestinal tract which is usually fatal. It is three to four times more prevalent in females. We present a case of a rare association of a male neonate with Megacystis Microcolon Intestinal Hypoperistalsis Syndrome who in addition had the classica...
متن کاملThe 11-13-week scan: diagnosis and outcome of holoprosencephaly, exomphalos and megacystis.
OBJECTIVE To determine the prevalence and outcome of fetuses with holoprosencephaly, exomphalos and megacystis diagnosed at 11-13 weeks of gestation. METHODS As part of a prospective screening study for trisomy 21 in singleton pregnancies at 11 + 0 to 13 + 6 weeks' gestation, transabdominal ultrasound examination was performed to diagnose holoprosencephaly, exomphalos and megacystis. Fetal ka...
متن کاملMegacystis at 10-14 weeks of gestation: chromosomal defects and outcome according to bladder length.
AIMS To examine the prevalence of chromosomal defects and outcome of fetuses with megacystis at 10-14 weeks of gestation. METHODS At the 10-14-week scan fetal megacystis was defined by a longitudinal bladder diameter of 7 mm or more. In 145 such fetuses the fetal karyotype and pregnancy outcome were examined in relation to the longitudinal diameter of the fetal bladder. RESULTS Chromosomal ...
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عنوان ژورنال:
- Urology journal
دوره 11 2 شماره
صفحات -
تاریخ انتشار 2014